Part of the signal cascade involved in glycogen degredation. Is phosphorylated by Protein Kinase A. Activates Phosphorylase b to Phosphorylase a.
Inactive form, found primarily in muscle in it's T state.
Active form, found primarily in the liver in its R state.
Phosphorylates glycogen which releases Glucose 1-Phosphate.
Gluconeogenic enzyme involved in dephosphorylating glucose 6-phosphate to glucose. Important in regulating blood sugar.
Converts Glucose 1-Phosphate to Glucose 6-Phosphate to proceed with glycolysis.
Phosphorylase deficiency. Results in hepatomegaly and hypoglycemia.
I Von Gierke Disease
Glucose 6-Phosphatase deficiency, none in the liver. Results in hepatomegaly, hypoglycemia, failure to thrive. Treat with starch and glucose enriched diet.