Case56: Severe Hearing Loss
Terms in this set (11)
If a 13 month old healthy boy presents with language delay and normal motor development, what it the likely diagnosis?
What is the next best step if hearing loss in a young child is suspected?
Evaluation by an audiologist
What is conductive hearing loss?
Hearing loss caused by disorders of the outer and middle ear
What is retrocochlear hearing loss?
Hearing loss caused be deficits in the auditory (vestibulocochlear) nerve or the central auditory nervous system
What is sensorineural hearing loss?
Hearing loss caused by disorders of the cochlea
What are some of the possible causes of sensorineural hearing loss?
It can either be caused by congenital or acquired factors. Congenital factors can be divided into genetic factors and prenatal infections
What are some of the genetic factors that can lead to sensorineural hearing loss?
Waardenburg syndrome (partial albino + deaf), branchio-oto-renal syndrome, Alport syndrome, Down syndrome, Jervell and Lange Nielson syndrome, and Hunter-Hurler syndromes
What are some of the neonatal infections that can lead to sensorineural hearing loss?
Cytomegalovirus (most common), toxoplasmosis, rubella, and syphilis
What are some conditions in the prenatal period that are associated with sensorineural hearing loss?
Prematurity, low APGAR score, low birth weight, mechanical ventilation for more than 5 days, hyperbilirubinemia, and bacterial meningitis
How can hearing adequacy be evaluated in children?
By asking their parents if they respond to sounds, and asking about language development
What is the best way to diagnose hearing impairments at birth in neonates?
Auditory brain-stem evoked response testing