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NSG 335 Final
Terms in this set (30)
What is Angelman Syndrome commonly misdiagnosed as?
Which chromosome is mutated in Angelman Syndrome?
What are some signs of Angelman Syndrome? (Select all that apply)
Seizures, speech impairment, ataxia of gait, and stiff or jerky movements
A nurse is caring for a 6 month old patient with late-stage Krabbe disease. Which intervention is a priority?
Raise the head of the bed 30 degrees
A family comes into the hospital with a child with an new diagnosis with Krabbe Disease. When assessing the need for psychological support for the family, which question will provide the most information?
"Can you tell me what has helped you cope with other stressful events in the past?"
A nurse is caring for a family whose child is on hospice because of Krabbe Disease. Which statement by the nurse is most accurate about hospice care?
Hospice care continues after the death of your child.
A patient experiencing a flare-up with Crohn's Disease is ordered complete bowel rest by the physician. You are administering TPN (total parenteral nutrition) per physician order. When developing the patient's nursing plan of care, which nursing diagnosis is MOST important to include in the care plan?
Risk for imbalanced nutrition: less than body requirements
A patient with Crohn's Disease is taking corticosteroids. The patient is complaining of extreme thirst, polyuria, and blurred vision. What is your next nursing action?
Check patient's blood glucose
A patient with Crohn's Disease is most likely to have the disease in what part of the GI tract?
A nurse is assessing a 22 month old child with suspected Toulouse-Lautrec syndrome. Which of the following would not be a symptom of this disease?
A parent brings in their child who has been diagnosed with Toulouse-Lautrec syndrome. Which statement shows the understanding of the teaching?
"I should take my child for regular check ups at the dentist."
A nurse instructs a parent with a child who has a diagnosis of Toulouse-Lautrec syndrome "to keep their home clutter free with few tripping hazards." What would be the best rationale for the nurse saying this?
The child is at high risk for fractures due to brittle bones.
How common is Marfan Syndrome?
What body systems does Marfan Syndrome affect?
Musculoskeletal, Cardiovascular, and respiratory
What causes Marfan's Syndrome?
Variety of mutations in the FBN1 gene
Cerebral palsy (CP) may result from a variety of causes. It is now known that the most common cause of CP is
prenatal brain abnormalities.
The major goal of therapy for children with cerebral palsy (CP) is
recognizing the disorder early and promoting optimal development.
A 3-year-old has cerebral palsy (CP) and is hospitalized for orthopedic surgery. The child's mother states the child has difficulty swallowing and cannot hold a utensil to self-feed. The child is slightly underweight for height. What is the most appropriate nursing action related to feeding?
Stabilize the child's jaw with one hand (either from a front or side position) to facilitate swallowing.
What are some signs and symptoms of Tay-Sachs Disease?
Muscle Weakness, Seizures, Cherry-red spot in eye
Who is most likely to get Tay-Sachs disease?
Tay-Sachs results from a mutation in which of the following?
What is the best way to treat thalassemia?
Who has the highest risk of inheriting the thalassemia trait?
What is the normal level of hemoglobin?
A patient is admitted to the pediatrics unit. Which statement made by the family regarding Trisomy 13 is not true?
Trisomy 13 is inherited
The family of an infant with Trisomy 13 has recently been admitted to the NICU. Which statement by the parents reflects effective coping related the patient's diagnosis?
"We will forever cherish these last few moments with our baby."
Which of the following are physical signs of Trisomy 13? (Select all that apply)
Hernias, Cleft lip or palate, Extra fingers/toes, Seizures
a nurse is caring for an infant who had a myelomenigocele. which of the following actions should the nurse include in the preoperative plan of care?
apply a sterile, moist dressing on the sac
a nurse is caring for an infant and notices an audible click in their left hip. which of the following diagnostic rest should the nurse expect the provider to preform?
Barlow test, ortolani test
a nurse is caring for a toddler who has hip dysplasia and has been placed in a hip spica cast. the Childs guardian asks the nurse why a pavlik harness is not being used. which of the following should the nurse make.
the pavlik harness is used for infant less than 6 months of age
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